SYSTEMIC VASCULITIS
Vasculitis:inflammation of B.V leading to end organ or tissue damage.
Primary vasculitides:
less common , serious ( fatal ) form are Wegner granulomatosis & Microscopic polyangitis
2ndry vasculitides:
to C.T dis. SLE, PSS , & Childhood DMS
D.DIAGNOSIS:
- Sepsis- Metastatic tumors
- Multiple emboli (Cholesterol, septic or thrombotic emboli)
Classification of primary vasculitis:
I. Large v. arteritis:1. Gaint cell arteritis
2. Takayasu arteritis .(pulse less dis.or aortic arch synd.)
II. Medium size v. arteritis:
1. Classical polyarteritis nodosa (PAN)
2. Kawasaki arteritis (Mucocutaneous L.N synd.)
III. Small size v.(arterioles, capillaries & vennules ):
1. Microscopic polyangitis.
2.Wegner s granulomatosis.
3.Churg Strauss synd.
4. Leukocytoclastic vasculitis.
5. Henoch – Schonlein purpura.
6. Essential mixed cryoglobulinemia.
Ideal Group
A.H.Yahia